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What is Childhood Neurofibrosarcoma?

  • Neurofibrosarcoma, also known as peripheral nerve sheath tumor, is a type of soft tissue tumor that develops in the cells surrounding the peripheral nerves. Peripheral nerves are nerves that receive messages from the central nervous system (brain and spinal cord) leading them to stimulate voluntary movement. Neurofibrosarcoma can sometimes arise in patients with neurofibromatosis (NF1).

    Neurofibrosarcoma is usually found in the arms and legs and can spread extensively along nerve tissue. It usually does not metastasize (spread) to other parts of the body, although it sometimes spreads to the lungs.

    Neurofibrosarcoma treatment at Dana-Farber/Boston Children's

    Children diagnosed with neurofibrosarcoma are treated through the Bone and Soft Tissue Tumor Program at Dana-Farber/Boston Children's Cancer and Blood Disorders Center. Our specialists — including pediatric oncologists, surgical oncologists and radiation oncologists — offer a level of expertise in soft tissue tumors rarely seen at other pediatric cancer centers. We provide the full set of options that can be used to treat fibrosarcoma, and our specialists can help you determine which option is best for your child.

    Learn more about neurofibrosarcoma

    Find in-depth information on neurofibrosarcoma on the Dana-Farber/Boston Children's website, including details on neurofibrosarcoma symptoms, diagnosis and treatment.